Test Entry - Detail

Familial Hypercholesterolaemia Genetic Screen


General
  Clinical Use: Full testing includes massively parallel sequencing of cardiometabolic genes with targeted analysis of hypercholesterolaemia genes (LDLR, APOB, PCSK9, APOE, LDLRAP1, LIPA, ABCG5, ABCG8). Please indicate on the request form the indication for testing.
MBS criteria (index case - full testing) -Test requested by a specialist or consultant physician, for a patient: (a) for whom no familial mutation has been identified; and (b) who has any of the following: (i) a Dutch Lipid Clinic Network score of at least 6; (ii) an LDL cholesterol level of at least 6.5 mmol/L in the absence of secondary causes; (iii) an LDL cholesterol level of between 5.0 and 6.5 mmol/L with signs of premature or accelerated atherogenesis.
MBS criteria (family cascade testing) -Detection of a familial mutation for a patient who has a first or second degree relative with a documented pathogenic germline gene variant for familial hypercholesterolaemia.
  Availability: As required.
  Aliases/Synonyms: FH (Familial Hypercholesterolaemia Genetic Screen),   Hypercholesterolaemia (FH Genetic Screening),   LDL Receptor Mutation Screening,   LDLR (FH Genetic Screening),   Sitosterolaemia,  
  Code: BFHGS
  Handling Instructions (to laboratory): Send sample ambient.
  Hyperlink:
  Reference Interval:
Not Applicable


Collection Requirements
  Container: EDTA (LAVENDER),  
  Sample Type: Blood; Extracted DNA
  Minimum Collection Volume:
  Collection Instructions:


Processing Requirements
  Alternate Containers:
  Processing Instructions:
  Minimum Assay Volume:
  Stability: 3 days ambient
  Transport Instructions (to testing laboratory): Send sample ambient.


Testing Locations
  Performed at:
Section Department Site Contact Phone
Cardiovascular Genetics Biochemistry Fiona Stanley Hospital 6152 8128


Last Updated : 07-10-2020 11:13