Test Entry - Detail

Familial Hypocalciuric Hypercalcaemia (FHH) Genetic Test


General
  Clinical Use: For the diagnosis of FHH and to distinguish FHH from primary hyperparathyroidism and other disorders of calcium homeostasis.
Patient must have proven PTH-dependent hypercalcaemia with urine calcium uncharacteristically low for primary hyperparathyroidism.
Sequence analysis of CASR (FHH1), exons 2 to 7 of GNA11 (FHH2) and exon 2 of AP2S1 (FHH3).
  Availability:
  Aliases/Synonyms: Calcium Receptor Mutation,   CASR,   FHH,  
  Code: BFHHG
  Handling Instructions (to laboratory): Send sample ambient.
  Hyperlink:
  Reference Interval:
Refer to report or laboratory


Collection Requirements
  Container: EDTA (LAVENDER),  
  Sample Type: See container
  Minimum Collection Volume:
  Collection Instructions:


Processing Requirements
  Alternate Containers:
  Processing Instructions: Store sample at room temperature.
  Minimum Assay Volume:
  Stability: 3 days ambient
  Transport Instructions (to testing laboratory): Send sample ambient.


Testing Locations
  Performed at:
Section Department Site Contact Phone
Cardiovascular Genetics Biochemistry Fiona Stanley Hospital 6152 8128


Last Updated : 03-10-2020 08:15